The initial report of a patient with visceral scleroderma without skin involvement was published in 1954, [1] and in 1962, the term "progressive systemic sclerosis sine scleroderma" was coined.

Objective To develop a model that assesses the risk for progressive disease in patients with systemic sclerosis (SSc) over the short term, in order to guide clinical management. Methods Baseline ...

Thomas's Hospital, London. Three patients with the unusual combinations of discoid lupus, systemic lupus erythematosus (SLE), and progressive systemic sclerosis (PSS) are reported. The first patient ...

Interstitial lung disease associated with diffuse systemic sclerosis. Management ... as treatments for severe, rapidly progressive ILD in the setting of diffuse SSc. There is currently no proven ...

A case is reported of progressive systemic sclerosis with pulmonary fibrosis which was complicated by recurrent haemoptyses due to diffuse pulmonary haemorrhage. We have found no other report of this ...

More specifically the following search strategy was followed: (‘systemic sclerosis’/exp OR ‘generalised scleroderma’ OR ‘generalized scleroderma’ OR ‘progressive scleroderma’ OR ‘progressive ...

Background Systemic sclerosis (SSc), like all chronic autoimmune disorders, may be complicated by AA amyloidosis (AAa). An associated B-cell lymphoma my cause amyloid λ or κ light-chain deposition and ...

Because it is rare (the incidence rate for the systemic form is estimated to be 19 new cases per year per 1 million adults), many nurses and physicians have only read about scleroderma.

So, what do the symptoms look like? Systemic scleroderma, also known simply as scleroderma, is a chronic connective tissue ...

A 65-year-old woman with a 35-year history of limited cutaneous systemic scleroderma was admitted to our hospital complaining of a 3-month history of progressive dyspnoea on exertion. High-resolution ...